Development of bilateral dural arteriovenous fistulae following pial synangiosis for moyamoya syndrome: case report.
Publication/Presentation Date
7-1-2019
Abstract
Moyamoya syndrome predisposes patients to ischemic or hemorrhagic stroke due to progressive narrowing of intracranial vessels with subsequent small-vessel collateralization. Dural arteriovenous fistulae (DAVFs) are most commonly noted after venous sinus or cortical vein thrombosis and are believed to be primarily due to venous hypertension and elevated sinus pressures, although there is no known association with moyamoya syndrome, or with surgical treatment for moyamoya disease (MMD). The authors present the case of a 14-year-old girl with Down syndrome treated using pial synangiosis for MMD who subsequently was noted to have bilateral DAVFs. This case provides a new perspective on the origins and underlying pathophysiology of both moyamoya syndrome and DAVFs, and also serves to highlight the importance of monitoring the moyamoya population closely for de novo cerebrovascular changes after revascularization procedures.
Volume
24
Issue
1
First Page
9
Last Page
13
ISSN
1933-0715
Published In/Presented At
Koduri, S., Wilkinson, D. A., Griauzde, J. M., Gemmete, J. J., & Maher, C. O. (2019). Development of bilateral dural arteriovenous fistulae following pial synangiosis for moyamoya syndrome: case report. Journal of neurosurgery. Pediatrics, 24(1), 9–13. https://doi.org/10.3171/2019.2.PEDS18603
Disciplines
Medicine and Health Sciences
PubMedID
30978680
Department(s)
Department of Surgery
Document Type
Article