Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report.
Publication/Presentation Date
6-1-1996
Abstract
Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifactorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasia) who has a documented family history of two sisters with lichen sclerosus et atrophicus. She presented with vulvar pruritus in association with dyspareunia, and biopsy of atrophic white vulvar lesions was consistent with lichen sclerosus et atrophicus. Lichen sclerosus et atrophicus has been previously noted to occur in association with morphoea and lichen planus, although it has never been reported in conjunction with CREST syndrome.
Volume
134
Issue
6
First Page
1144
Last Page
1146
ISSN
0007-0963
Published In/Presented At
Fitzgerald, E. A., Connelly, C. S., Purcell, S. M., & Kantor, G. R. (1996). Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report. The British journal of dermatology, 134(6), 1144–1146.
Disciplines
Medicine and Health Sciences
PubMedID
8763444
Department(s)
Department of Medicine
Document Type
Article