Primary synovial sarcoma of the lung with intra-cardiac extension.

Publication/Presentation Date

1-1-2011

Abstract

Synovial sarcomas are a distinct clinical entity occurring most often in the lower extremities. They account for 10-14% of all soft tissue sarcomas. Pulmonary synovial sarcomas are quite rare and account for less than 0.5% of all intra-thoracic neoplasms. We present the first reported case of primary pulmonary synovial sarcoma with intra cardiac extension in a 53-year-old male who presented with chronic cough. Imaging revealed a large right upper lobe mass extending through the superior pulmonary veins into the left atrium. The patient underwent a right total pneumonectomy with extraction of the left atrial mass and left atrial reconstruction. Pathology and immunohistochemistry was diagnostic of primary pulmonary synovial sarcoma positive for SYT-SSX1 gene fusion transcription.

Volume

81

Issue

3

First Page

249

Last Page

252

ISSN

1423-0356

Disciplines

Medicine and Health Sciences

PubMedID

20714127

Department(s)

Department of Medicine

Document Type

Article

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