Rosai-Dorfman disease with massive intracranial involvement: asymmetric response to conservative therapy.
Publication/Presentation Date
4-1-2011
Abstract
Rosai-Dorfman Disease (RDD) is a rare, idiopathic lymphoproliferative disorder. Central nervous system (CNS) involvement in this disorder is an uncommon manifestation. The clinical and radiographic appearance of CNS RDD is variable, and may mimic more common diseases. Treatment is controversial, and spontaneous remission is common. Positive outcomes have been reported with radiation therapy, or corticosteroid administration, or surgical excision. Our case is unusual in that the extracranial sites of involvement responded to corticosteroid therapy while the intracranial masses progressed.
Volume
21
Issue
2
First Page
194
Last Page
196
ISSN
1552-6569
Published In/Presented At
Walker, R. N., Nickles, T. P., Lountzis, N. I., Jacobs, D. L., & Nawaz, N. K. (2011). Rosai-Dorfman disease with massive intracranial involvement: asymmetric response to conservative therapy. Journal of neuroimaging : official journal of the American Society of Neuroimaging, 21(2), 194–196. https://doi.org/10.1111/j.1552-6569.2009.00404.x
Disciplines
Medicine and Health Sciences
PubMedID
19659569
Department(s)
Department of Medicine
Document Type
Article