Microangiopathy of brain, retina, and inner ear.

Publication/Presentation Date

3-1-1995

Abstract

Microangiopathy of brain, retina, and inner ear is a rare syndrome manifesting as arteriolar occlusions of the brain, retina, and inner ear, with resultant encephalopathy, visual, and hearing loss. Despite exhaustive laboratory examinations in these patients, no evidence of a systemic disease can be found. We treated and followed an adolescent with this disorder who initially presented with a branch retinal artery occlusion. A unique finding in this case was retinal vessel wall hyperfluorescence noted five days prior to retinal infarction. The patient developed recurrent branch artery occlusions, sensorineural hearing loss, and central nervous system infarctions despite anticoagulation and immunosuppressive treatment.

Volume

15

Issue

1

First Page

1

Last Page

8

ISSN

1070-8022

Disciplines

Medicine and Health Sciences

PubMedID

7780564

Department(s)

Department of Medicine

Document Type

Article

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