Acute myeloid leukemia in a patient with thrombocytopenia with absent radii: A case report and review of the literature.

Publication/Presentation Date

12-1-2018

Abstract

Thrombocytopenia with absent radii (TAR) syndrome is a rare congenital disorder characterized by low platelet counts of various severity, bilateral absent radii but thumbs are usually present. TAR syndrome is not generally associated with bone marrow failure or malignancy. Janus kinase-2, myeloproliferative leukemia protein, and calreticulin are not mutated in TAR patients. Only four cases of leukemia were reported in TAR patients in the literature: three acute myeloid leukemia (AML) and one acute lymphoblastic leukemia. Of the three cases of AML found in TAR patient, only one was reported in an adult. We report a case of myelodysplastic syndrome progressing to AML with calreticulin driver mutation in an adult male with TAR syndrome who was successfully treated with hematopoietic allogeneic stem cell transplantation.

Volume

11

Issue

4

First Page

245

Last Page

247

ISSN

2589-0646

Disciplines

Medicine and Health Sciences

PubMedID

28259746

Department(s)

Department of Medicine, Lehigh Valley Topper Cancer Institute

Document Type

Article

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