Linear IgA Bullous Dermatosis Preceding the Diagnosis of Primary Sclerosing Cholangitis and Ulcerative Colitis: A Case Report.
Publication/Presentation Date
7-1-2019
Abstract
Linear IgA bullous dermatosis (LABD) is a rare autoimmune blistering disorder seen in the pediatric and adult populations that is often linked to a medication, infection, or underlying gastrointestinal, hepatobiliary, or autoimmune disease. In this study, we describe the case of a 23-year-old white man whose presentation and diagnosis of LABD ultimately led to the discovery of underlying primary sclerosing cholangitis (PSC) and ulcerative colitis (UC). His dermatitis resolved with topical steroids and dapsone, and he is undergoing systemic treatment for his UC and PSC. This exceptional case further validates the association between LABD with UC, strengthens that with PSC, and underscores the importance of alerting clinicians to consider conducting a systemic workup in addition to thorough medication history on making the diagnosis of LABD.
Volume
41
Issue
7
First Page
498
Last Page
501
ISSN
1533-0311
Published In/Presented At
Humphrey, V. S., Lee, J. J., Supakorndej, T., Malik, S. M., Huen, A. C., & Jaroslaw, J. (2019). Linear IgA Bullous Dermatosis Preceding the Diagnosis of Primary Sclerosing Cholangitis and Ulcerative Colitis: A Case Report. The American Journal of dermatopathology, 41(7), 498–501. https://doi.org/10.1097/DAD.0000000000001313
Disciplines
Medicine and Health Sciences
PubMedID
30461424
Department(s)
Department of Medicine
Document Type
Article
