Heterozygous ATR mutations in mismatch repair-deficient cancer cells have functional significance.

Publication/Presentation Date

8-15-2005

Abstract

ATR (ataxia telangiectasia and Rad3-related) function is necessary for the proper response to commonly used chemotherapeutic agents. Heterozygous truncating mutations in exon 10 of the ATR gene have been described in numerous cancers exhibiting microsatellite instability. We show that truncating mutations of ATR are capable of acting in a dominant-negative manner to abrogate ATR-dependent Chk1 phosphorylation and cell-cycle arrests after DNA damage. In addition, endometrial cell lines harboring ATR mutations are defective for ATR-dependent responses. These findings imply that ATR mutations play an important role in the development and clinical behavior of a subset of microsatellite instability-positive endometrial, colon, and stomach cancers.

Volume

65

Issue

16

First Page

7091

Last Page

7095

ISSN

0008-5472

Disciplines

Medicine and Health Sciences

PubMedID

16103057

Department(s)

Department of Obstetrics and Gynecology

Document Type

Article

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