Paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome: Part II. Diagnosis and management.
Publication/Presentation Date
7-1-2024
Abstract
In the second part of this Continuing Medical Education article on paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome (PNP/PAMS), its diagnostic criteria, investigative work-up, and management are reviewed. PNP/PAMS is a rare autoimmune blistering disorder associated with high morbidity and mortality. Recognizing PNP/PAMS's key features and its diagnostic criteria is critical in initiating appropriate work-up. Evaluating PNP/PAMS requires knowledge of its findings on histopathology, direct immunofluorescence, indirect immunofluorescence, and enzyme-linked immunosorbent assay. Lastly, treatments for PNP/PAMS are reviewed with suggestions based on case reports and expert opinions in the literature.
Volume
91
Issue
1
First Page
13
Last Page
22
ISSN
1097-6787
Published In/Presented At
Huang, S., Anderson, H. J., & Lee, J. B. (2024). Paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome: Part II. Diagnosis and management. Journal of the American Academy of Dermatology, 91(1), 13–22. https://doi.org/10.1016/j.jaad.2023.08.084
Disciplines
Medicine and Health Sciences
PubMedID
37714216
Department(s)
Department of Pathology and Laboratory Medicine
Document Type
Article