Pigmented epithelioid melanocytoma: a rare lytic bone lesion involving intradural extension and subtotal resection in a 14-month-old girl.
Publication/Presentation Date
6-1-2020
Abstract
Pigmented epithelioid melanocytomas (PEMs) are low-grade, intermediate-type borderline melanocytic tumors with limited metastatic potential. To date, PEMs have been treated via gross-total resections. Postoperative recurrence and mortality are rare. This case highlights a unique presentation of a PEM that involved bone destruction and intradural infiltration, which required a subtotal resection. To the authors' knowledge, this is the first report of a PEM extending through the dura and necessitating subtotal resection, which is contrary to the standard of care, gross-total resection. Surveillance imaging 10 months after resection remained negative for clinical and radiological recurrence.
Volume
25
Issue
6
First Page
625
Last Page
628
ISSN
1933-0715
Published In/Presented At
D'Souza, P., Barr, E. K., Thirumala, S. D., Jacob, R., & Nagy, L. (2020). Pigmented epithelioid melanocytoma: a rare lytic bone lesion involving intradural extension and subtotal resection in a 14-month-old girl. Journal of neurosurgery. Pediatrics, 25(6), 625–628. https://doi.org/10.3171/2020.1.PEDS19359
Disciplines
Diagnosis | Medicine and Health Sciences | Other Analytical, Diagnostic and Therapeutic Techniques and Equipment | Radiology
PubMedID
32168491
Department(s)
Department of Radiology and Diagnostic Medical Imaging
Document Type
Article