A rare case of Rosai-Dorfman disease presenting as a pulmonary artery mass in a 33-year-old female with hypoxia.
Publication/Presentation Date
4-1-2023
Abstract
Rosai-Dorfman disease (RDD) is a rare form of non-Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID-19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately.
Volume
13
Issue
2
First Page
12214
Last Page
12214
ISSN
2045-8932
Published In/Presented At
Dronamraju, V., McSurdy, K., Graham, R., Rali, P., Kumaran, M., Proca, D., Lashari, B., Toyoda, Y., & Gupta, R. (2023). A rare case of Rosai-Dorfman disease presenting as a pulmonary artery mass in a 33-year-old female with hypoxia. Pulmonary circulation, 13(2), e12214. https://doi.org/10.1002/pul2.12214
Disciplines
Diagnosis | Medicine and Health Sciences | Other Analytical, Diagnostic and Therapeutic Techniques and Equipment | Radiology
PubMedID
37007934
Department(s)
Department of Radiology and Diagnostic Medical Imaging
Document Type
Article