Atypical presentation of extranodal Rosai-Dorfman disease.
Publication/Presentation Date
2-1-2009
Abstract
We describe a 42-year-old woman with progressive dyspnea on exertion resulting from pulmonary artery compression by a mediastinal mass due to extranodal Rosai-Dorfman disease. After initial biopsies were inconclusive, she underwent surgical resection of the mass to relieve the pulmonary artery compression, which was causing severe right ventricular dysfunction. Debulking of the mass required resection and reconstruction of the ascending aorta, pulmonary trunk, and bilateral pulmonary arteries using cardiopulmonary bypass and circulatory arrest. We believe this is the first report of Rosai-Dorfman disease manifesting as compression of the thoracic great vessels.
Volume
87
Issue
2
First Page
616
Last Page
618
ISSN
1552-6259
Published In/Presented At
Prendes, B. L., Brinkman, W. T., Sengupta, A. L., & Bavaria, J. E. (2009). Atypical presentation of extranodal Rosai-Dorfman disease. The Annals of thoracic surgery, 87(2), 616–618. https://doi.org/10.1016/j.athoracsur.2008.07.037
Disciplines
Medicine and Health Sciences
PubMedID
19161795
Department(s)
Department of Surgery
Document Type
Article