Syndromic scoliosis in a patient with arthrochalasia Ehlers-Danlos syndrome corrected with a Wood-Rigo-Cheneau derotational brace.
Publication/Presentation Date
9-28-2024
Abstract
We present a boy in middle childhood with a medical history of arthrochalasiaEhlers-Danlos syndrome who was diagnosed with scoliosis as a toddler. His treatment began at a regional children's hospital, where initial spine radiographs demonstrated a 43.6° dextroscoliosis curve with the apex at L3. He was initially treated with a Boston brace, and the family was informed that MAGEC (Magnetic Expansion Control) growing rods were likely the definitive treatment due to the high likelihood of progression given the patient's large Cobb angle. However, the decision was made by the family and the Ehlers-Danlos syndrome specialist to proceed with the Wood-Rigo-Cheneau derotational brace.
Volume
17
Issue
9
ISSN
1757-790X
Published In/Presented At
Brown, M., Krasney, L., & Lavallee, M. (2024). Syndromic scoliosis in a patient with arthrochalasia Ehlers-Danlos syndrome corrected with a Wood-Rigo-Cheneau derotational brace. BMJ case reports, 17(9), e259469. https://doi.org/10.1136/bcr-2023-259469
Disciplines
Medicine and Health Sciences
PubMedID
39343458
Department(s)
Department of Surgery
Document Type
Article