Cruveilhier-Baumgarten disease in a patient with Turner syndrome: case report of a rare indication for liver transplantation.

Authors

Federico Aucejo
Zuhaib Ibrahim MDFollow
Koji Hashimoto
Cristiano Quintini
Dympna Kelly
David Vogt
Bijan Eghtesad
John Fung
Charles Miller
Ralph Tuthill

Publication/Presentation Date

3-1-2008

Abstract

Some chromosomal alterations can be associated with vascular abnormalities. For instance, Turner syndrome can be complicated by agenesis or hypoplasia of the portal venous system causing presinusoidal portal hypertension. Liver transplantation to treat this condition overcomes portal hypertension and reconstitutes the diminished hepatic function due to severe atrophy of the portal venous inflow.

Volume

14

Issue

3

First Page

299

Last Page

302

ISSN

1527-6473

Published In/Presented At

Aucejo, F., Ibrahim, Z., Hashimoto, K., Quintini, C., Kelly, D., Vogt, D., Eghtesad, B., Fung, J., Miller, C., & Tuthill, R. (2008). Cruveilhier-Baumgarten disease in a patient with Turner syndrome: case report of a rare indication for liver transplantation. Liver transplantation : official publication of the American Association for the Study of Liver Diseases and the International Liver Transplantation Society, 14(3), 299–302. https://doi.org/10.1002/lt.21374

Disciplines

Medicine and Health Sciences

PubMedID

18306332

Department(s)

Department of Surgery

Document Type

Article