Airway manifestations of inflammatory bowel disease are rare in pediatrics. This case describes a nine-year-old female with ulcerative colitis (UC) with progressive stridor and dyspnea for two months. Severe upper airway obstruction was noted on spirometry. CatScan (CT) of the neck and chest revealed tracheal narrowing with circumferential, heterogeneous soft tissue thickening, and posterior wall nodularity. Bronchoscopy visualized the granulation tissue of the large airways and an ulcerative lesion to the right mainstem. Consultation and evaluation by gastroenterology, oncology, and rheumatology determined a diagnosis of extraintestinal manifestations of UC. Systemic steroids led to symptom resolution and improvement in lung function.
Published In/Presented At
Kuntzman K, Chennupati SK, Tolaymat N, Bingham CA, Greenawald L. Progressive stridor: extraintestinal airway manifestations in a pediatric patient with inflammatory bowel disease. Clin J Gastroenterol. 2022 Aug 2. doi: 10.1007/s12328-022-01674-w. Epub ahead of print. PMID: 35917109.
Medicine and Health Sciences | Pediatrics
Department of Pediatrics, Department of Pediatrics Faculty, Department of Pediatrics Residents