Congenital Left Atrial Mitral Accessory Chord With Accessory Mitral Valve Tissue Causing Dual-Valve Regurgitation.
Publication/Presentation Date
12-2-2025
Abstract
BACKGROUND: Left atrial mitral valve (MV) accessory chord and accessory MV tissue are rare congenital anomalies that may mimic more common pathologies.
CASE SUMMARY: A 30-year-old man presented with dyspnea, weight loss, and an outpatient transthoracic echocardiogram concerning for infective endocarditis. Transesophageal echocardiography revealed a chordlike structure extending from the limbus of the interatrial septum to the anterior MV leaflet, continuing through the left ventricular outflow tract, across the aortic valve, and into the ascending aorta. These findings were associated with moderate mitral regurgitation and severe aortic regurgitation. Surgical resection confirmed the diagnosis of accessory MV tissue with a left atrial MV accessory chord.
DISCUSSION: Patients may present with heart failure or malperfusion symptoms due to valvopathy or left ventricular outflow tract obstruction. Multimodal imaging and surgical resection with valve repair are key to diagnosis and management.
TAKE-HOME MESSAGES: Chordal anomalies can mimic endocarditis and cause dual-valve disease. Early transesophageal echocardiography and surgical intervention are critical to avoid misdiagnosis.
First Page
106222
Last Page
106222
ISSN
2666-0849
Published In/Presented At
Sabri, M. S., Waqar, F., Mizrahi, E., Fireman, A., Watson, R., West, J. L., & Garrido, M. (2025). Congenital Left Atrial Mitral Accessory Chord With Accessory Mitral Valve Tissue Causing Dual-Valve Regurgitation. JACC. Case reports, 106222. Advance online publication. https://doi.org/10.1016/j.jaccas.2025.106222
Disciplines
Medicine and Health Sciences
PubMedID
41329103
Department(s)
Fellows and Residents
Document Type
Article