Using selective laser trabeculoplasty to manage glaucoma in a child with phakomatosis pigmentovascularis.
Publication/Presentation Date
6-1-2026
Abstract
PURPOSE: To describe the management and complications associated with using selective laser trabeculoplasty (SLT) to treat elevated intraocular pressure (IOP) in a child with phakomatosis pigmentovascularis (PPV).
OBSERVATIONS: A 13-year-old female with bilateral cutaneous hemangiomas of the face and lower limb length discrepancy presented with elevated IOP in the right eye despite maximal medical glaucoma management. There was no evidence of buphthalmos, Haab's striae, posterior embryotoxon, or anterior segment dysgenesis. Initial nerve fiber layer and visual field testing confirmed structural and functional damage, respectively. Genetic testing confirmed a variant in the guanine nucleotide-binding protein G(q) subunit alpha (
CONCLUSIONS AND IMPORTANCE: Glaucoma filtering procedures in cases of PPV pose a high risk of complications and SLT offers a less-invasive, potentially clinic-based alternative. While the patient did develop a choroidal effusion post-SLT, suspected to be secondary to decreased IOP, this resolved with medical management alone without the need for incisional surgery thus illustrating both the risks and benefits of SLT in treating patients with phakomatoses-associated glaucoma.
Volume
42
First Page
102555
Last Page
102555
ISSN
2451-9936
Published In/Presented At
Bai, P., Ruiz, K. C., Wang, C., Oatts, J. T., & Abbasian, J. (2026). Using selective laser trabeculoplasty to manage glaucoma in a child with phakomatosis pigmentovascularis. American journal of ophthalmology case reports, 42, 102555. https://doi.org/10.1016/j.ajoc.2026.102555
Disciplines
Medicine and Health Sciences | Pediatrics
PubMedID
41890785
Department(s)
Department of Pediatrics
Document Type
Article