Hepatobiliary cystadenoma: a rare pediatric tumor.
Publication/Presentation Date
8-1-2013
Abstract
Hepatobiliary cystadenoma is a rare hepatic neoplasm that has been reported only 10 times in the pediatric population. Although considered a benign cystic tumor of the liver, hepatobiliary cystadenoma has a high risk of recurrence with incomplete excision and a potential risk for malignant degeneration. Complete tumor excision with negative margins is the mainstay in treatment. Unfortunately, due to the paucity of cases and its vague presentation, hepatobiliary cystadenoma is rarely diagnosed preoperatively. Therefore, in patients with hepatic cystic masses without a clear diagnosis, total resection of the lesion with negative margins is indicated to adequately evaluate for malignant potential and limit the risk of recurrence. We describe a 2-year-old girl with an asymptomatic abdominal mass that was found to be hepatobiliary cystadenoma. In addition, the pathogenic, histopathologic and clinical features of hepatobiliary cystadenoma are reviewed.
Volume
29
Issue
8
First Page
841
Last Page
845
ISSN
1437-9813
Published In/Presented At
Tran, S., Berman, L., Wadhwani, N. R., & Browne, M. (2013). Hepatobiliary cystadenoma: a rare pediatric tumor. Pediatric surgery international, 29(8), 841–845. https://doi.org/10.1007/s00383-013-3290-z
Disciplines
Medicine and Health Sciences | Pediatrics
PubMedID
23483342
Department(s)
Department of Pediatrics
Document Type
Article