Cardiac tumor in juvenile onset Behçet's disease: case report and review of the literature.
Publication/Presentation Date
2-1-2010
Abstract
Behçet's disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet's disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart's right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.
Volume
31
Issue
2
First Page
277
Last Page
279
ISSN
1432-1971
Published In/Presented At
Adams, E. E., Aluquin, V. P., Bingham, C. A., Stone, J. R., & Pauliks, L. B. (2010). Cardiac tumor in juvenile onset Behçet's disease: case report and review of the literature. Pediatric cardiology, 31(2), 277–279. https://doi.org/10.1007/s00246-009-9565-4
Disciplines
Medicine and Health Sciences | Pediatrics
PubMedID
19859764
Department(s)
Department of Pediatrics
Document Type
Article